Torsión esplénica / Splenic Torsion

Introducción: El síndrome de torsión se incluye dentro de los síndromes que causan abdomen agudo quirúrgico. Como causa poco frecuente de este síndrome se encuentra la torsión esplénica en bazos que tienen anomalía en su fijación. Objetivo: Informar sobre la evolución de una paciente tratada por torsión de un bazo errante. Presentación del caso: Paciente de ocho años de edad, femenina, de color no blanco de la piel, con antecedentes de dolor abdominal crónico recurrente, que acudió al Servicio de Urgencias del Hospital Pediátrico de Cienfuegos Paquito González Cueto con dolor abdominal agudo, intermitente, de 48 horas de evolución, vómitos, abdomen doloroso a la palpación profunda en cuadrante superior izquierdo y masa palpable en flanco lateral del mismo lado de tres cm. Se sospechó una torsión esplénica. Se realizó, como complementario diagnóstico ultrasonido abdominal Doppler y tomografía contrastada de abdomen. Se hizo laparotomía y se encontró bazo torcido, con cambios de coloración por la isquemia, que recuperó su color normal después de la destorsión. Se fijó el órgano a la pared abdominal. La evolución posquirúrgica resultó satisfactoria. Conclusiones: La torsión esplénica, aunque infrecuente, debe sospecharse en pacientes con dolor intermitente y masa palpable, principalmente en flanco lateral izquierdo. La tomografía contrastada resulta el examen diagnóstico de elección y se requiere de un diagnóstico temprano para poder conservar el bazo, órgano muy importante para una mejor función inmunológica en los niños(AU)

Introduction: Torsion syndrome is included among the syndromes causing acute surgical abdomen. A rare cause of this syndrome is splenic torsion in spleens with abnormal fixation. Objective: To report on the evolution of a patient treated for torsion of an errant spleen. Case presentation: Eight-year-old female patient, non-white skin color, with a history of recurrent chronic abdominal pain, who attended the Emergency Department of the Paquito González Cueto Pediatric Hospital of Cienfuegos with intermittent acute abdominal pain of 48 hours of evolution, vomiting, painful abdomen on deep palpation in the left upper quadrant and palpable mass in the lateral flank of the same side measuring three centimeters. Splenic torsion was suspected. Doppler abdominal ultrasound and contrasted tomography of the abdomen were performed as a complementary diagnosis. Laparotomy was performed and the spleen was found to be twisted, with changes in color due to ischemia, which recovered its normal color after detorsion. The organ was fixed to the abdominal wall. The postoperative evolution was satisfactory. Conclusions: Splenic torsion, although rare, should be suspected in patients with intermittent pain and palpable mass, mainly in the left lateral flank. Contrast tomography is the diagnostic test of choice and early diagnosis is required to preserve the spleen, a very important organ for better immune function in children(AU)

The left gastro-omental vessels are able to maintain the entire spleen blood supply / Os vasos gastromentais esquerdos são capazes de manter o suprimento sanguíneo de todo o baço

Abstract The spleen is supplied by blood flow through the splenic artery and vein. The purpose of this communication is to report an ectopic spleen supplied only by reverse flow through the left gastro-omental vessels. A 14-year-old boy presented with pelvic splenomegaly supplied only by the left gastro-omental artery and veins connected to the inferior polar vessels, which were the only vessels communicating with the spleen. After detorsion of the spleen and splenopexy, the spleen returned to normal dimensions. The patient had uneventful follow-up. In conclusion, the left gastroepiploic vessels are able to maintain the entire spleen blood supply.

Resumo O baço é suprido pelo fluxo sanguíneo da artéria e veia esplênicas. O objetivo desta comunicação é apresentar um baço ectópico suprido apenas pelo fluxo sanguíneo reverso proveniente dos vasos gastromentais esquerdos. Um paciente de 14 anos apresentou esplenomegalia pélvica suprida apenas por artéria e veia gastromentais esquerdas, conectadas aos vasos polares inferiores, que eram os únicos presentes nesse baço. Após a distorção do baço e a esplenopexia, o baço voltou às dimensões normais. Não houve intercorrências no acompanhamento do paciente. Em conclusão, os vasos gastromentais esquerdos são capazes de suprir o fluxo sanguíneo de todo o baço.

Torsión esplénica con localización inusual, reporte de caso / Splenic torsion with unusual location, case report

Resumen El bazo errante es una entidad clínica muy poco frecuente en niños, representando menos del 0.25% de todas las esplenectomías. Puede ocurrir por la ausencia congénita de ligamentos suspensorios del bazo, o debido a una laxitud adquirida de los mismos. El espectro clínico va desde condición asintomática con hallazgo incidental, hasta presentación de abdomen agudo. El conocimiento de esta condición y de sus hallazgos radiológicos, juegan un papel esencial para lograr un diagnóstico correcto y tratamiento quirúrgico oportuno. La preservación del bazo más esplenopexia es el procedimiento de elección. Se presenta un paciente de 4 años con antecedente de cirugía antirreflujo, en quien se encontró bazo ectópico errante con torsión esplénica, que fue manejado exitosamente con conservación del bazo y esplenopexia. MÉD.UIS.2021;34(1): 113-18

Abstract Wandering spleen is an uncommon clinical entity in children, representing less than 0,25% of all splenectomies. It is caused by laxity or absence of the supporting splenic ligaments. Its clinical spectrum varies from asymptomatic disease with incidental finding to acute abdominal pain due to torsion. The knowledge of this condition and its radiological findings plays a crucial role in reaching the correct diagnosis and timely surgical treatment. Spleen preservation with splenopexy is recognized as the procedure of choice. We report a case of a four year old patient with a history of anti-reflux surgery, with a wandering spleen and splenic torsion, successfully managed with spleen conservation and splenopexy. MÉD.UIS.2021;34(1): 113-18

Wandering spleen as a cause of sinistral portal hypertension

Wandering spleen (WS) is a rare entity characterized by laxity of peritoneal ligaments that hold the spleen stationary. It is most commonly diagnosed in children and young women. Clinical presentation ranges from asymptomatic to acute abdomen. A 19-year-old woman came to the emergency department with history of progressive abdominal pain. She also had previous episodes of hematemesis. A computed tomography scan showed an ectopic spleen with a "whirlpool sign." Laparotomy and splenectomy were performed. WS is characterized by a long vascular pedicle and laxity of peritoneal attachments of the spleen. The etiology is usually congenital. Splenopexy is the main treatment; however, splenectomy is indicated when splenic infarction is present. Despite being rare, this condition may be considered in some cases of abdominal pain. An earlier diagnosis would have allowed us to perform a splenopexy, thus reducing morbidity. (AU)

Wandering Spleen as a Cause of Acute Abdomen: A Surgical Conundrum from Acute Appendicitis to Splenic Torsion and Ischemic Small Bowel Volvulus

@#Wandering spleen is renowned as a surgical enigma due to its diverse presentations. Due to lack of its attaching ligaments which would usually place it at the left hypochondrium region, the spleen ‘wanders’ and may be located anywhere within the abdominal cavity. This condition has been associated with many complications such as splenic torsion, pancreatitis and portal hypertension. We report a case of a wandering spleen presenting as acute appendicitis in an 18-year-old young active sportsman. The patient developed post-operative ileus and later intestinal obstruction which necessitated exploratory laparatomy onto which the final diagnosis of splenic and small bowel infarct due to splenic torsion with small bowel volvulus was made. Splenectomy, small bowel resection and primary anastomosis were performed and the patient made a full recovery.

Bazo errante: una causa infrecuente de abdomen agudo / Wandering spleen: an unusual cause of acute abdomen

El síndrome de bazo errante es una condición infrecuente en la cual existe ausencia o hiperlaxitud en los elementos de fijación esplénicos que predispone a una ubicación inusual en el abdomen y mayor riesgo de torsión e infarto visceral. Su etiología puede ser congénita o adquirida y la presentación clínica es variable. El diagnóstico se basa en sospecha clínica, laboratorio y estudios por imágenes. La cirugía es el único tratamiento definitivo para esta afección. Presentamos el caso de una mujer de 23 años de edad con antecedentes de episodios recurrentes de dolor en hipocondrio izquierdo desde la infancia. Al examen físico se encontraba hemodinámicamente estable, afebril y con dolor en hipocondrio izquierdo. La ecografía mostró esplenomegalia homogénea y la tomografía de abdomen evidenció un bazo aumentado de tamaño, de posición conservada, con arremolinamiento y congestión de los vasos en el hilio esplénico. Se interpretó el cuadro como isquemia esplénica secundaria a torsión del pedículo vascular. Se realizó laparoscopia exploradora que evidenció bazo de 18 cm libre en hipocondrio izquierdo, con venas varicosas en la periferia y sin ligamentos de fijación. Se realizó esplenectomía por vía laparoscópica. La anatomía patológica informó necrosis isquémica del órgano. Evolucionó favorablemente con alta hospitalaria al tercer día postoperatorio.

Wandering spleen syndrome is a rare condition in which absence or laxity of splenic fixing elements predisposes to an unusual location in the abdomen and an increasing risk of twisting and infarction. Its etiology may be congenital or acquired and clinical presentation is variable. Diagnosis is based on clinical suspicion, laboratory and imaging. Surgery is the only definitive treatment for this pathology. We report the case of a 23 year old woman with a history of recurrent episodes of abdominal pain in the left upper quadrant since childhood. On physical examination she was afebrile, hemodynamically stable, with marked abdominal tenderness in the left upper quadrant. Ultrasonography showed homogeneous splenomegaly. Abdominal CT-scan presented an enlarged, eutopic spleen, with swirling and congestion of hilum vessels. Splenic ischemia due to organ torsion was suspected. Exploratory laparoscopy was performed showing an 18 cm in diameter spleen free in left upper quadrant, with varicose veins in the periphery and without fixing ligaments. Laparoscopic splenectomy was completed. The pathology report showed ischemic necrosis of the organ. The patient progressed favorably and was discharged on the third postoperative day.

Torsion of the wandering spleen and pancreatic tail precipitating diabetic ketoacidosis in a patient with Prader Willi Syndrome: A case report / Journal of the ASEAN Federation of Endocrine Societies

@#Prader Willi Syndrome (PWS) includes complex endocrinological issues because of the hypothalamic and pituitary dysfunction which include obesity and diabetes, as well as behavioural issues. Other important aspects of PWS, such as hepatosplenomegaly are sometimes neglected. We present a case of diabetic ketoacidosis precipitated by torsion of a wandering spleen in a 22-year-old woman with PWS and type 2 diabetes mellitus. The pancreatic tail was involved in the torsion leading to hyperamylasaemia and pancreatitis. The splenic torsion and pancreatitis were initially treated conservatively with resolution of symptoms. A year later, she had another 2 episodes of severe abdominal pain due to worsening splenic torsion which subsided with conservative management. She subsequently underwent an elective splenectomy which revealed an enlarged and wandering spleen, with 720 degrees torsion of the long splenic pedicle.

Wandering Spleen- A diagnostic Challenge: Case Report and Review of Literature

Wandering spleen or hypermobile spleen results from the elongation or maldevelopment of the spleen’s suspensory ligaments. It is a rare clinical entity that mainly affects children. Among adults, it is most commonly found in females of active reproductive age. It may present as an asymptomatic mass in the abdomen, or it may present with intermittent abdominal discomfort because of torsion and spontaneous detorsion of the spleen. We present the case of a 37-year-old female who had features of intestinal obstruction with mass per abdomen. Exploratory laparotomy showed an infarcted spleen. A total splenectomy was performed.

MR Images of Infarction of Wandering Spleen Associated with Intestinal Non-rotation

Wandering spleen is a rare clinical condition caused by lax splenic suspensory ligaments. The laxity of ligaments causes torsion of splenic vascular pedicle. CT scan of a 7-year-old girl with abdominal pain showed a non-enhancing lobular mass in lower abdomen. Small bowel loops were located at the right-sided abdomen and colonic loops at the left-sided abdomen. MRI scan showed non-enhancing heterogeneous mass with twisted vascular pedicle. To our knowledge, only a few cases have been reported about wandering spleen diagnosed on MRI.

Wandering Spleen: An Unusual Association with Gastric Volvulus

Gastric volvulus is a rare disease; only 700 cases have been reported since Berti first described autopsy findings of a patient in 1866. Its symptoms are non-specific and therefore it is difficult to diagnose it early. Acute gastric volvulus has a poor prognosis because it may cause shock and strangulation. Perforation or gastric hemorrhage can also result from ischemia when diagnosis is delayed. Therefore, it requires rapid diagnosis and an emergency operation. Wandering spleen is a rare condition characterized by the absence or underdevelopment of one or all of the ligaments that hold the spleen in its normal position in the abdomen. Wandering spleen and gastric volvulus have a common cause lack of intraperitoneal visceral ligaments. The authors now report a case of wandering spleen accompanying gastric voluvulus, which resulted in wandering spleen and perforation.

Baço migratório em hérnia paraestomal / Wandering spleen in parastomal hernia

The authors report a case of a parastomal hernia that incarcerated a wandering spleen. We present a very rare case of an 85-year-old woman with a giant parastomal hernia. Computed tomography revealed a parastomal hernia with a wandering spleen inside. We introduce a different and simple alternative approach, with the smallest inconvenience as possible to solve the trouble. We carried out the treatment with a prosthetic repair closing the defect with ePTFE mesh, performed through a laparoscopic approach, intraperitoneal, like a tie and move the spleen back to its anatomical place. The result was excellent.

Splenic Infarction due to Torsion of Wandering Spleen: A Case Report

Wandering spleen is very rare condition in children characterized by migration of the spleen from its normal position due to laxity or absence of the supporting splenic ligaments. We experienced a case of splenic infarction due to torsion of a wandering spleen in a 6-year-old boy who presented with fever, vomiting, and abdominal pain of 2 day's duration. On physical examination, there was severe tenderness in the left upper quadrant of the abdomen. The plain abdominal radiograph showed marked colonic gaseous distension. Contrast-enhanced abdominal computed tomography scan showed decreased density of spleen in the normal position, consistent with infarction. At emergency laparotomy, a wandering spleen twisted 360degrees on its pedicle was found. Despite splenic detorsion, blood flow could not be restored. Splenectomy was therefore performed. The child was discharged 7 days after surgery without any complications.

A Case of Wandering Spleen in a Patient Who Presented at the ED with Mild Abdominal Pain in the Left Upper Quadrant

A wandering spleen is a rare entity characterized by incomplete fixation of the spleen by lienorenal and gastrosplenic ligaments. The spleen can migrate to the lower abdomen or pelvis and the condition can be congenital or acquired. We report a case of torsion of a wandering spleen in a patient presenting with progressing mild left upper quadrant pain.

Acute Torsion of a Wandering Spleen Managed by Splenopexy / 대한혈액학회지

Torsion of the spleen is a rare cause of abdominal pain in children and it may occur in conjunction with wandering spleen. Wandering spleen is the presence of the spleen in a location other than the left upper quadrant, and it is secondary to the congenital or functional absence of splenic ligaments. The occurrence of wandering spleen is rare in adults and it's even less common in children. The most common presentation is acute abdominal pain, although the signs and symptoms vary widely. Due to the risk of splenic infarction, making a rapid and accurate diagnosis is essential. When a wandering spleen is diagnosed, the treatment of choice is splenopexy, even if the patient is asymptomatic. If splenic necrosis is present, then splenectomy is usually required. We describe here a 4-year-old girl with torsion of a wandering spleen that was managed by splenopexy.

A Case of Wandering Spleen / 대한소아소화기영양학회지

Wandering spleen is a rare condition characterized by migration of the spleen from its normal position due to laxity or absence of the supporting splenic ligaments. Ultrasonography shows the absence of the spleen in left upper quadrant (LUQ) and the presentation in the lower abdomen of a homognous mass whose sonographic appearance is consistent with that of a spleen. Contrast-enhanced CT reveals the absence of the spleen in LUQ, a soft tissue mass resembling spleen in the lower abdomen, and the splenic pedicle of whirled appearance. We present a case of wandering spleen, which could be diagnosed with US and CT by the ectopic location of spleen and the whirling pattern of splenic pedicle.

Infarction of Wandering Spleen with Torsion of Its Pedicle: A case report

Torsion of a wandering spleen is an unusual cause of an acute abdomen and is rarely diagnosed preoperatively. A splenectomy is the treatment of choice in cases of splenic torsion and infarction, while in patients with chronic symptoms, splenopexy may be attempted. I report a case with acute splenic infarction in a young male and review the clinical presentation, etiology, diagnostic procedures and treatment modalities in a wandering spleen.

Splenopexy for Wandering Spleen with Torsion in a Child

Torsion of the wandering spleen is a rare condition especially in children. Unfortunatly, splenectomy was the advocated treatment of choice for wandering spleen in many children up to 1985 in spite of the well-known possibility of overwhelming postsplenectomy sepsis. Because of the conclusive evidence of the vital function of the spleen in infection, indication of splenectomy have been revised and more attention has been paid to preserving the spleen where possible. We are presented a girl with splenic torsion, seen as a migratory abdominal mass and intermittent vague abdominal pain. Splenopexy by fixation of the spleen to the diaphragm and posterolateral peritoneum and the use of A vitene in the splenic bed was successfully performed. Complete fixation of the spleen was confirmed by ultrasound a year after this procedure was carried out. The clinical pesentation, etiology, diagnostic procedures and management are discussed also.

A case of Wandering spleen

No abstract available.